Melkersson–Rosenthal Syndrome with Isolated Immunoglobulin E Hypogammaglobulinaemia

Idiopathic Acquired Hypogammaglobulinaemia with Melanosis, Associated with Sibship Immunoglobulin Abnormalities and Ankylosing Spondylitis.

Dementia in a patient with Thymoma and hypogammaglobulinaemia (Good's syndrome)

Good's syndrome is extremely rare and refers to an acquired B and T cell immunodeficiency in thymoma patients. The authors of this article present a case report of a 75-year-old, caucasian male patient previously subjected to examinations for secondary dementia and recurrent infections, which revealed paraneoplastic syndrome arose from thymoma. He underwent thymectomy, while his immunodeficienc...

Pathogenesis of hypogammaglobulinaemia with thymoma and late-onset hypogammaglobulinaemia.

Hypogammaglobulinaemia with Whipple's disease.

The patient, a 54-year-old housewife, was well until the age of 40 years when she developed repeated infections. During the next 10 years recurrent attacks of diarrhoea also appeared and were associated with weight loss, increased skin pigmentation, and later the occurrence of arthralgia and polyserositis. She was found to have deficiencies of IgG and IgA. A malabsorption syndrome was establish...

Importace of monoclonal immunoglobulin in Sjögren’s syndrome

Background: Sjögren’s syndrome is the second most common systemic autoimmune disease after rheumatoid arthritis, RA, with a prevalence of about 0.5% in the general population. It occurs primarily in perimenopausal women (at a ratio of women to men of 9: 1) Sjögren’s syndrome is characterized by lymphocytic infiltration to exocrine glands. The specific autoantibodies of this syndrome are against...